snímek PPT
Hereditary elliptocytosis
Mild anemia, in combination with other
anemizing factors only
Again a membrane defect of actin-
spectrin-ankyrin skeleton
No therapy
Defects in erythrocyte metabolism
G6-PD deficiency anemia
95% of all glucose metabolism enzyme
deficiencies
Triggering factors: oxidizing drugs,
infections (? activation of leucocytes
producing active oxygen radicals)
Favism is a unique phenomenon – fava
beans (contain an oxidant L-dopa)